Long-Term Study of Cerebral Glucose Metabolism in Huntington's Disease
Primary Purpose
Huntington's Disease
Status
Completed
Phase
Locations
Study Type
Observational
Intervention
Sponsored by
About this trial
This is an observational trial for Huntington's Disease focused on measuring Huntington's disease, neurologic and psychiatric disorders, rare disease
Eligibility Criteria
PROTOCOL ENTRY CRITERIA: --Disease Characteristics-- Documented family history of Huntington's disease (HD) Symptomatic HD: chorea required At-risk for HD: no detectable systemic or oculomotor abnormality Age-matched control subjects No history of inherited neurological disease No general or neurologic abnormality --Prior/Concurrent Therapy-- At least 4 weeks since other HD treatment, e.g.: Haloperidol Benzodiazepine Other tranquilizers or neuroleptics --Patient Characteristics-- No pregnant women
Sites / Locations
Outcomes
Primary Outcome Measures
Secondary Outcome Measures
Full Information
NCT ID
NCT00004753
First Posted
February 24, 2000
Last Updated
June 23, 2005
Sponsor
National Center for Research Resources (NCRR)
Collaborators
National Institute of Neurological Disorders and Stroke (NINDS), University of California, Los Angeles
1. Study Identification
Unique Protocol Identification Number
NCT00004753
Brief Title
Long-Term Study of Cerebral Glucose Metabolism in Huntington's Disease
Study Type
Observational
2. Study Status
Record Verification Date
December 2001
Overall Recruitment Status
Completed
Study Start Date
August 1993 (undefined)
Primary Completion Date
undefined (undefined)
Study Completion Date
undefined (undefined)
3. Sponsor/Collaborators
Name of the Sponsor
National Center for Research Resources (NCRR)
Collaborators
National Institute of Neurological Disorders and Stroke (NINDS), University of California, Los Angeles
4. Oversight
5. Study Description
Brief Summary
OBJECTIVES: I. Correlate clinical outcome with cerebral glucose metabolism in patients with Huntington's disease (HD) and their at-risk relatives.
II. Evaluate the efficacy of cerebral glucose metabolism in observing the pathophysiologic development of HD, monitoring responses to experimental therapy, and predicting HD genotype.
III. Identify, define, and describe the natural history of pathophysiologic lesions in HD.
IV. Characterize the genotypic and phenotypic expression of the HD gene.
Detailed Description
PROTOCOL OUTLINE: Participants are screened for Huntington's disease, including cerebral glucose metabolism assessment and genetic testing.
Studies include a detailed family history and neurologic, psychometric, and neurobehavioral evaluations. Imaging includes positron emission tomography with fluorodeoxyglucose and brain magnetic resonance imaging.
A genotype assessment is performed; genetic results are not disclosed to patients or relatives.
6. Conditions and Keywords
Primary Disease or Condition Being Studied in the Trial, or the Focus of the Study
Huntington's Disease
Keywords
Huntington's disease, neurologic and psychiatric disorders, rare disease
7. Study Design
Enrollment
90 (false)
10. Eligibility
Sex
All
Minimum Age & Unit of Time
0 Years
Accepts Healthy Volunteers
Accepts Healthy Volunteers
Eligibility Criteria
PROTOCOL ENTRY CRITERIA:
--Disease Characteristics--
Documented family history of Huntington's disease (HD)
Symptomatic HD: chorea required
At-risk for HD: no detectable systemic or oculomotor abnormality
Age-matched control subjects
No history of inherited neurological disease
No general or neurologic abnormality
--Prior/Concurrent Therapy--
At least 4 weeks since other HD treatment, e.g.:
Haloperidol
Benzodiazepine
Other tranquilizers or neuroleptics
--Patient Characteristics--
No pregnant women
Overall Study Officials:
First Name & Middle Initial & Last Name & Degree
John C. Mazziotta
Organizational Affiliation
University of California, Los Angeles
Official's Role
Study Chair
12. IPD Sharing Statement
Learn more about this trial
Long-Term Study of Cerebral Glucose Metabolism in Huntington's Disease
We'll reach out to this number within 24 hrs