Physical Training Introduction in Lifestyle of Facioscapulohumeral Dystrophy Patients (FSHD1)
Muscular Dystrophy, Facioscapulohumeral
About this trial
This is an interventional treatment trial for Muscular Dystrophy, Facioscapulohumeral focused on measuring Muscular Dystrophy, Facioscapulohumeral, Physical training, Exercise
Eligibility Criteria
Inclusion Criteria:
- facioscapulohumeral dystrophy
- Being capable of supporting an exercise on ergocycle
- Social Security regimen affiliated
- Consent form signed
Exclusion Criteria:
- Severe cardiac or respiratory insufficiency
- Cardiac pacemaker
- Morbid obesity (BMI upper to 35)
- Anti platelet therapy
Sites / Locations
- CHU de Grenoble
- CHU de Saint-Etienne
Arms of the Study
Arm 1
Arm 2
Experimental
Other
Physical training
control
The training will consist in 3 sessions of 35 min of training per week at home on an ergocycle. As a result, lower limb muscles will be mainly solicited. These muscles are heterogeneous in terms of deficiency, but this latter is compatible with cycling. The training will be divided in (i) 2 sessions of 30 min aerobic exercises at a constant but moderate (60% of maximal aerobic power, MAP) intensity followed with 5 sets of 10 revolutions at near-maximal intensity and (ii) an interval-training session. This latter session will consist in 5 min warm-up at 40% MAP followed by 5 times 1 min at 80% MAP (recovery = 4 min at 40% MAP) followed by 5 min of active recovery. Over a 2 to 4 weeks initial period, the program will be conducted in the laboratory or at home under the supervision of a coach. Then a systematic supervision of the sessions by the coach will be performed by phone, by using the heart rate recordings and values of Analogic Visual Scale for pain and fatigue.
None intervention