Effect of Eleclazine on Shortening of the QT Interval, Safety, and Tolerability in Adults With Long QT Syndrome Type 3
Long QT Syndrome Type 3
About this trial
This is an interventional treatment trial for Long QT Syndrome Type 3 focused on measuring Type 3 long QT syndrome (LQT3), Long QT syndrome, Congenital long QT, Sudden cardiac death
Eligibility Criteria
Key Inclusion Criteria:
- Individuals with an established diagnosis of LQT3 (by genotype testing)
- Mean (of triplicate) QTc interval ≥ 480 msec (or ≥ 460 msec, for individuals who are currently taking ranolazine or Class I antiarrhythmic drugs such as mexiletine) at 3 or more time points, determined by standard 12-lead ECG, at screening
Key Exclusion Criteria:
- Known mutations associated with type 1 long QT syndrome (LQT1) or type 2 long QT syndrome (LQT2)
- Known or suspected history of seizures or epilepsy
- History of heart failure defined as New York Heart Association (NYHA) Class IV and/or known left ventricular ejection fraction (EF) ≤ 45%
- Body mass index (BMI) ≥ 40 kg/m^2 at screening
- Severe renal impairment at screening (defined as an estimated glomerular filtration rate (eGFR) < 30 mL/min/1.73m^2, using the 4 Variable Modification of Diet in Renal Disease (MDRD) equation, as determined by the study center)
- Abnormal liver function tests at screening, defined as alanine aminotransferase (ALT) or aspartate aminotransferase (AST) > 2 x upper limit of normal (ULN), or total bilirubin > 1.5 x ULN
- An aborted cardiac arrest (ACA), implantable cardioverter-defibrillator (ICD) implantation, syncopal episode, or appropriate ICD therapy within 3 months prior to screening
- Any other condition or circumstance that in the opinion of the investigator would preclude compliance with the study protocol
Note: Other protocol defined Inclusion/Exclusion criteria may apply.
Sites / Locations
- Mayo Clinic Rochester
- NYU Langone Medical Center
- University of Rochester Medical Center
- Nova Scotia Health Authority
- L'institut Du Thorax Nantes
- Groupe Hospitalier Bichat Claude Bernard
- CHU Réunion Sud
- LMU Klinikum der Universität München
- Tel Aviv Sourasky Medical Center
- Fondazione Salvatore Maugeri IRCCS
- Academisch Medisch Centrum Amsterdam
- Barts and The London School of Medicine and Dentistry
Arms of the Study
Arm 1
Arm 2
Experimental
Experimental
Eleclazine (Single-blind treatment phase)
Open-label Extension Phase
Eleclazine and/or eleclazine placebo up to Week 24
Eligible participants will continue to receive open-label eleclazine until this drug is commercially available for the treatment of patients with LQT3, or until Gilead terminates development of eleclazine for the treatment of patients with LQT3, or the investigator deems it no longer in the participant's best interest.