Standardized Treatment of Pulmonary Exacerbations II (STOP2)
Pulmonary Cystic Fibrosis
About this trial
This is an interventional treatment trial for Pulmonary Cystic Fibrosis focused on measuring Cystic fibrosis, Pulmonary exacerbation, Antibiotic, Treatment duration, Lung infection, Cystic Fibrosis Foundation, Cystic Fibrosis Foundation National Patient Registry
Eligibility Criteria
Inclusion Criteria:
Key Inclusion Criteria:
- Male or female ≥18 years of age at Visit 1
- Documentation of a CF diagnosis
- Enrolled in the Cystic Fibrosis Foundation National Patient Registry (CFFNPR) prior to Visit 1 (US sites only)
- At the time of Visit 1, there is a plan to initiate IV antibiotics for a pulmonary exacerbation
- Performed spirometry at Visit 1 and Visit 2 and willing to perform spirometry at Visit 3
- Completed the CRISS questionnaire at Visit 1 and Visit 2 and willing to complete the Cystic Fibrosis Respiratory Symptoms Diary (CFRSD) questionnaire at Visit 3
- Willing to adhere to a specific treatment duration determined by initial response to treatment and subsequent randomization
- Willing to return for follow up Visit 3
- Written informed consent obtained from the subject or subject's legal representative
Exclusion Criteria:
Key Exclusion Criteria
- Previous randomization in this study
- Treatment with IV antibiotics in the 6 weeks prior to Visit 1
- Admission to the intensive care unit for current pulmonary exacerbation in the two weeks prior to Visit 2, unless admission was due to a desensitization protocol
- Pneumothorax in the two weeks prior to Visit 2
- Primary diagnosis for current hospitalization is unrelated to worsening lower respiratory symptoms (e.g., pulmonary clean out, distal intestinal obstruction syndrome (DIOS), sinusitis)
- Massive hemoptysis defined as > 250 cc in a 24 hour period or 100 cc/day over 4 consecutive days occurring in the two weeks prior to Visit 2
- Current pulmonary exacerbation thought to be due to allergic bronchopulmonary aspergillosis (ABPA)
- At Visit 1, receiving ongoing treatment with a duration of more than 2 weeks with prednisone equivalent to >10mg/day
- History of solid organ transplantation
- Receiving antimicrobial therapy to treat non-tuberculous mycobacterium (e.g., M. abscessus, M. avium complex) in the two weeks prior to Visit 2
Sites / Locations
- The Children's Hospital Alabama
- Providence Alaska Medical Center
- University Medical Center
- UC San Diego Medical Center
- Lucile S. Packard Children's Hospital
- University of California Davis, Health System
- National Jewish Health
- Hartford Hospital
- Yale New Haven Hospital
- Shands Hospital
- Joe DiMaggio Children's Hospital (Adult)
- University of Miami
- Emory University Hospital
- Augusta University Medical Center
- St. Luke's Regional Medical Center
- Saint Francis Medical Center
- Indiana University Hospital, Indiana University Health
- The University of Kansas Hospital
- John Hopkins Hospital
- Boston Children's Hospital (BCH)
- University of Massachusetts Memorial Health Care (Worcester, MA)
- University of Michigan Health System
- Detroit Medical Center; Harper University Hospital
- Saint Louis University Hospital
- St. Louis Washington University Adult - Barnes-Jewish Hospital
- Billings Clinic
- Dartmouth Hitchcock Medical Center
- Monmouth Medical Center
- Morristown Medical Center
- Robert Wood Johnson University Hospital (New Brunswick, NJ)
- Women and Children's Hospital of Buffalo
- The Long Island Jewish Medical Center
- Beth Israel Medical Center
- Columbia University Medical Center
- Highland Hospital; Strong Memorial Hospital
- SUNY Upstate Medical University Hospital
- New York Medical College
- North Carolina Children's Hospital
- Wake Forest University Baptist Medical Center
- Akron Children's Hospital
- University Hospital of Cleveland
- Nationwide Children's Hospital
- Dayton Children's Hospital
- Penn State Milton S. Hershey Medical Center
- Hospital of the University of Pennsylvania
- Children's Hospital of Pittsburgh of UPMC
- Medical University of South Carolina; Medical University of South Carolina Children's Hospital
- University of Texas Southwestern
- Baylor St. Lukes Medical Center
- University of Texas Health Center at Tyler
- The University of Vermont Medical Center Inc.
- University of Virginia Health System
- Medical College of Virginia (Richmond, VA)
- University of Washington Medical Center
- Ruby Memorial Hospital
- University of Wisconsin Hospital Center
- Froedtert Hospital
- Calgary Canada Adult CF Clinic
Arms of the Study
Arm 1
Arm 2
Arm 3
Arm 4
Other
Other
Other
Other
ERR-10
ERR-14
NERR-14
NERR-21
ERR treatment duration - 10 Day Standard of care IV antibiotic(s) will be selected by the treating physician. Duration of treatment is the assigned intervention.
ERR treatment duration - 14 Day Standard of care IV antibiotic(s) will be selected by the treating physician. Duration of treatment is the assigned intervention.
NERR treatment duration - 14 Day Standard of care IV antibiotic(s) will be selected by the treating physician. Duration of treatment is the assigned intervention.
NERR treatment duration - 21 Day Standard of care IV antibiotic(s) will be selected by the treating physician. Duration of treatment is the assigned intervention.