User-centred Assistive System for Arm Functions in Neuromuscular Subjects (USEFUL)
Muscular Dystrophies, Muscular Dystrophy, Duchenne, Muscular Dystrophy, Becker
About this trial
This is an interventional supportive care trial for Muscular Dystrophies focused on measuring Assistive devices, Randomized controlled trial (RCT), Upper limbs, Robotic devices
Eligibility Criteria
Inclusion criteria
- signed informed consent (we will expose the family the aims of our study and carefully describe the need of compliance with them)
- diagnosis of muscular dystrophy (genetic, histological and biochemical if necessary),specifically with Duchenne, Becker and Limb Girdle type 2 muscular dystrophy. No muscle biopsy will be performed, except in case there is a diagnostic need.
- being wheelchair bound
- having a scoring at the MRC scale for upper limb at the deltoid, biceps, triceps brachii muscles ranging from 2 to 4.
Exclusion criteria
- presence of additional diseases (for example: family history of mental retardation, epilepsy, cerebral palsy)
- behavioral and psychiatric disturbances (emotional problems, depression)
- absence of compliance to the study of the family and the caregivers
Sites / Locations
- IRCCS E. Medea - La Nostra Famiglia
- Villa Beretta
Arms of the Study
Arm 1
Arm 2
Active Comparator
Active Comparator
Armon Ayura
Jaeco Wrex
Upper limb assistive device with active solutions for gravity compensation. Intervention: The upper limb exoskeleton is worn by the patient on the preferred arm, and it is used during daily life activities to support arm movements, particularly getting rid of gravity arm weight.
Upper limb assistive device with passive solutions for gravity compensation. Intervention: The upper limb exoskeleton is worn by the patient on the preferred arm, and it is used during daily life activities to support arm movements, particularly getting rid of gravity arm weight.