A Study to Evaluate the Safety, Tolerability, and Pharmacokinetics of a Single Dose of SRP-5051 (Vesleteplirsen) in Patients With Duchenne Muscular Dystrophy (DMD)
Muscular Dystrophy, Duchenne
About this trial
This is an interventional treatment trial for Muscular Dystrophy, Duchenne focused on measuring Duchenne Muscular Dystrophy, Exon Skipping, DMD, Exon 51, Ambulatory, Pediatric, Nonambulatory, Peptide-conjugated phosphorodiamidate morpholino oligomer (PPMO), Duchenne
Eligibility Criteria
Inclusion Criteria:
- Has a genetic diagnosis of DMD and an out-of-frame deletion mutation of the DMD gene amenable to exon 51 skipping treatment
- Has been on a stable dose of oral corticosteroids for at least 12 weeks prior to study drug administration with continued dosing of oral corticosteroids while participating in the study*, or has not received corticosteroids for at least 12 weeks prior to study drug administration and will not initiate dosing of oral corticosteroids while participating in the study
Exclusion Criteria:
- Has a left ventricular ejection fraction (LVEF) less than (<) 40 percent (%) based on an echocardiogram (ECHO) performed within 3 months prior to Screening or at the Screening visit
- Has a QT interval corrected with Fridericia's method (QTcF) >= 450 millisecond (msec) on the Screening electrocardiogram (ECG)
- Initiation or change of dosing (except for modifications to accommodate changes in weight) within 12 weeks prior to Screening and while participating in the study for any of the following: angiotensin-converting enzyme (ACE) inhibitors, angiotensin-receptor blocking agents (ARBs), beta-blockers, or potassium
- Requires antiarrhythmic and/or diuretic therapy for heart failure
- Forced vital capacity (FVC) <40% of predicted value within 3 months of Screening or at the Screening visit
- Known kidney disease or had an acute kidney injury within 6 months prior to Screening
- Treatment with eteplirsen or drisapersen within 6 months prior to Screening, or any experimental gene therapy for the treatment of DMD at any time
- Use of any herbal medication/supplement containing aristolochic acid
Other inclusion/exclusion criteria apply.
*The dose of steroids must remain constant except for modifications to accommodate changes in weight.
Sites / Locations
- Neuromuscular Research Center
- NW FL Clinical Research Group, LLC
- Rare Disease Research, LLC
- Ann & Robert H. Lurie Children's Hospital of Chicago
- University of Kansas Medical Center
- Children's Hospital of Pittsburgh of UPMC
- Children's Medical Center Dallas
- London Health Sciences Centre
Arms of the Study
Arm 1
Experimental
SRP-5051
Patients will be sequentially assigned to receive 1 of the 5 escalating dose levels of SRP-5051 on Day 1. Patients who complete the study and continue to meet safety eligibility criteria will have the opportunity to enroll in an open-label extension study to continue to receive SRP-5051.