An Open-label, Phase 1/2 Trial of Gene Therapy 4D-310 in Adults With Fabry Disease
Fabry Disease
About this trial
This is an interventional treatment trial for Fabry Disease focused on measuring Lysosomal Storage Diseases, Nervous System Brain Diseases, Metabolic, Inborn Brain Diseases, Metabolic Brain Diseases, Central Nervous System Diseases, Nervous System Diseases, Cerebral Small Vessel Diseases, Cerebrovascular Disorders, Vascular Diseases, Cardiovascular Diseases, Genetic Diseases, X-Linked, Inborn, Metabolic Diseases, Lipid Metabolism Disorders, Sphingolipidoses, Metabolism, Inborn Errors, Lipodoses, Lipid Metabolism
Eligibility Criteria
Inclusion Criteria:
- Male or female ≥ 18 years of age
- Pathogenic GLA mutation consistent with Fabry Disease
- Confirmed diagnosis of classic or late-onset Fabry disease
- Individuals on ERT must be on a stable dose for at least 6 months (and a minimum of 12 months total exposure) prior to study enrollment
- Agree to use highly effective contraception
Exclusion Criteria:
- Presence of high titer neutralizing antibody to 4D-310 capsid, or presence of high antibody titer to AGA
- eGFR <45 mL/min/1.73 m2
- Undergone kidney transplantation or currently on hemodialysis or peritoneal dialysis
- HIV, active or chronic hepatitis B or C,
- Evidence of liver disease, severe pulmonary disease or diabetes with poor glycemic control
- History of stroke or transient ischemic attack within the last 12 months, or other significant thromboembolic disease history (e.g. pulmonary embolism)
- Contraindication to systemic corticosteroid therapy or immunosuppressive therapy
- Chronic steroid use, defined as ≥ 3 months of oral corticosteroid use within the last 12 months.
- Moderately severe to severe cardiovascular disease or uncontrolled hypertension
- Left ventricular ejection fraction of <45% on echocardiogram (ECHO)
- Currently receiving investigational drug, device or therapy or having ever received gene therapy
- History of infusion related response to ERT or any adverse reaction leading to ERT discontinuation
- History of cancer within 2 years (exceptions include non-melanoma skin cancer, localized prostate cancer treated with curative intent)
- Pregnant or breast-feeding
Sites / Locations
- University of Alabama at Birmingham
- University of California at San Diego
- University of California at Los Angeles
- Emory University
- Hackensack University
- Children's Hospital of Pittsburgh of UPMC
- University of Utah
- Lysosomal & Rare Disorders Research & Treatment Center, Inc
Arms of the Study
Arm 1
Arm 2
Arm 3
Arm 4
Experimental
Experimental
Experimental
Experimental
4D-310 Dose Level 1 - AAV Neutralizing Antibody (NAb) Group A
4D-310 Dose Level 1 - AAV NAb Titer Group B
4D-310 Dose Level 2 - AAV NAb Titer Group A and/or B
4D-310 Dose Expansion
Single IV administration of 4D-310 Dose Level 1 - AAV NAb Titer Group A patients
Single IV administration of 4D-310 Dose Level 1 - AAV NAb titer Group B patients
Single IV administration of 4D-310 at Dose Level 2 in AAV NAb titer Group A and/or B patients
Dose expansion cohort of single IV administration of 4D-310 at the selected dose and selected AAV Nab titer group(s) patients