A Phase 1 Study of VX-522 in Participants With Cystic Fibrosis (CF)
Cystic Fibrosis
About this trial
This is an interventional treatment trial for Cystic Fibrosis
Eligibility Criteria
Key Inclusion Criteria: Body mass index is less than (<) 30.0 kilograms per meter square (kg/m^2) A total body weight greater than (>) 50 kg Stable CF disease CFTR gene mutations on both alleles that are not responsive to CFTR modulator therapy o Example mutations include but are not limited to, mutations that do not produce CFTR protein (i.e., Class I): nonsense mutations (e.g., G542X, W1282X) and canonical splice mutations (e.g., 621+1G->T) Forced expiratory volume in 1 second (FEV1) value, percent of predicted mean for age, sex, and height (equations of the Global Lung Function Initiative [GLI])18 ≥40% Key Exclusion Criteria: History of uncontrolled asthma within a year prior to screening History of solid organ or hematological transplantation Hepatic cirrhosis with portal hypertension, moderate hepatic impairment (Child Pugh Score 7 to 9), or severe hepatic impairment (Child Pugh Score 10 to 15) Arterial oxygen saturation on room air less than (<) 94% at screening Other protocol defined Inclusion/Exclusion criteria may apply.
Sites / Locations
- University of Alabama at BirminghamRecruiting
- Miller Children's Hospital / Long Beach MemorialRecruiting
- Stanford UniversityRecruiting
- National Jewish HealthRecruiting
- University of Florida, Shands HospitalRecruiting
- University of Kansas Medical CenterRecruiting
- Baltimore - Early Phase Clinical UnitRecruiting
- Johns Hopkins HospitalRecruiting
- Massachusetts General Hospital Cystic Fibrosis Center Clinical Research CenterRecruiting
- Boston Children's HospitalRecruiting
- University of MinnesotaRecruiting
- Washington University School of Medicine / St. Louis Children's HospitalRecruiting
- Columbia University Medical CenterRecruiting
- University of CincinnatiRecruiting
- Rainbow Babies and Children's Hospital/University Hospitals Cleveland Medical CenterRecruiting
- Nationwide Children's HospitalRecruiting
- UPMC Children's Hospital of PittsburghRecruiting
- Medical University of South CarolinaRecruiting
- Vanderbilt University Medical CenterRecruiting
- University of UtahRecruiting
- University of Wisconsin Hospital and ClinicsRecruiting
- Royal Papworth Hospital NHS Foundation TrustRecruiting
- Clinical Research Facility, Queen Elizabeth University HospitalRecruiting
- Royal Brompton HospitalRecruiting
- Southampton General HospitalRecruiting
Arms of the Study
Arm 1
Experimental
VX-522
Participants will receive a single dose of different dose levels of VX-522.