ARTEMIS-PH - Study of Ambrisentan in Subjects With Pulmonary Hypertension Associated With Idiopathic Pulmonary Fibrosis (ARTEMIS-PH)
Idiopathic Pulmonary Fibrosis, Pulmonary Hypertension
About this trial
This is an interventional treatment trial for Idiopathic Pulmonary Fibrosis focused on measuring Idiopathic Pulmonary Fibrosis, Pulmonary Hypertension, PH, IPF, Ambrisentan, ERA, Endothelin Receptor Antagonist, Cardiovascular
Eligibility Criteria
Selected Inclusion Criteria:
- Weight ≥ 40 kg at screening
- Diagnosis of IPF based on modified American Thoracic Society-European Respiratory Society guidelines
- Diagnosis of PH based on the following hemodynamic requirements: mean pulmonary artery pressure (mPAP ≥ 25 mm Hg; pulmonary vascular resistance > 240 dyne.sec/cm^5; pulmonary capillary wedge pressure or left ventricular end-diastolic pressure ≤ 15 mm Hg
- Forced vital capacity (FVC) ≥ 40%
- Able to walk at least 50 meters during two 6-minute walk tests
- If receiving calcium channel blockers, low-dose oral corticosteroids, immunosuppressive, cytoxic, or antifibrotic drugs dose must have been stable.
Selected Exclusion Criteria:
- Diagnosis of PH primarily due to an etiology other than IPF
- Surgical lung biopsy diagnosis other than Usual Interstitial Pneumonia
- Other known cause of interstitial lung disease
- Evidence of significant obstructive lung disease
- Recent hospitalization for an acute exacerbation of IPF
- Recent active pulmonary or upper respiratory tract infection
- Left ventricular ejection fraction < 40%
- Serum creatinine ≥ 2.5 mg/dL
- Required hemodialysis, peritoneal dialysis, or hemofiltration
- Female subject who was pregnant or breastfeeding
- Recent treatment for PH with an endothelin receptor antagonist (ERA), phosphodiesterase type 5 inhibitor, or prostacyclin derivative
- Recent treatment with high dose oral corticosteroids
- Recent treatment (within 4 weeks prior to screening) with imatinib mesylate (Gleevec)
- Alanine aminotransferase or aspartate aminotransferase lab value that was greater than 1.5 x the upper limit of the normal range
- Discontinued other ERA treatment for any adverse reaction other than those associated with liver function test abnormalities
Sites / Locations
- University of Alabama at Birmingham
- Mayo Clinic Arizona
- University of California Davis
- David Geffen School of Medicine UCLA
- University of California San Diego Medical Center
- University of California at San Francisco
- Stanford University
- University of Colorado Heatlh Sciences Center
- Bay Area Chest Physicians
- University of Florida
- University of Miami Medical Center
- Suncoast Lung Center
- Sarasota Memorial Hospital
- Cleveland Clinic Florida
- Atlanta Institute for Medical Research
- University of Chicago
- Kentuckiana Pulmonary Association
- Maine Medical Center
- Johns Hopkins University School of Medicine
- Tufts Medical Center
- Brigham and Women's Hospital
- Boston University Medical Center
- Beth Israel Deacones Medical Center
- University of Michigan Health Systems
- Mayo Clinic Rochester
- Washington University
- Creighton University Center for Allergy & Asthma
- Dartmouth Medical School
- Albany Medical Center
- Winthrop University Hospital
- North Shore Health System
- Mount Sinai School of Medicine
- Columbia University
- University of North Carolina at Chapel Hill
- Duke University Medical Center
- The Lindner Center for Research & Education at The Christ Hospital
- University Hospitals of Cleveland Case Western
- Cleveland Clinic Foundation
- Ohio State University
- Hospital of the University of Pennsylvania
- Temple University School of Medicine
- Alleghany General Hospital
- University of Pittsburgh Cancer Institute
- Medical University of South Carolina
- Vanderbilt University Medical Center
- University of Texas Southwestern
- Baylor College of Medicine
- University of Utah
- Inova Heart Institiute and Vascular Institute
- Virginia Commonwealth University Health System
- Providence Everett Medical Center
- St. Vincents Hospital
- The Prince Charles Hospital
- Royal Perth Hospital
- Medizinische Universität Graz
- Universitatsklinikum Innsbruck
- Medizinische Universität Wien
- Peter Loughheed Center- Calgary General Hospital
- University of British Columbia
- London Health Sciences Centre
- Toronto General Hospital
- Centre Hospitalier De L'Universite de Montreal
- Sir Mortimer B. Davis Jewish General Center
- Centre de Pneumologie de L'Hospital Laval
- Evangelische Lungenklinik Berlin
- Charite-Universitatsmedizin Berlin
- Krankenhaus Donaustauf der LVA
- Universitatsklinikum Freiburg
- Universitat Greifswald
- Medizinische Hochschule Hannover
- Thorax Klinik
- LMU Klinikum der Universitat
- Azienda Ospedaliero Universitaria
- Presidio Ospedaliero G.B. Morgagni
- Unita Funzionale di Pneumologia e Fisiopatologia Respiratoria
- Ospedale S.Giuseppe Fatebenefratelli
- Azienda Ospedaliera di Padova
- Instituto Mediterraneo per i Trapianti e Terapie ad Alta Specializzazione
- Policlinico Universitario Tor Vergata
- Azienda Ospedaliera Universitaria Senese
- Centro delle Interstiziopatie Polmonari e Malattie Rare del Polmone
- Papworth Hospital NHS Foundation Trust
- University Hospital Aintree
- University College Hosptial
- Royal Hallamshire Hospital
Arms of the Study
Arm 1
Arm 2
Experimental
Placebo Comparator
Ambrisentan
Placebo
Participants were randomized to receive ambrisentan treatment at an initial dose of 5 mg for 4 weeks, followed by ambrisentan at the target dose of 10 mg for an additional 52 weeks
Participants were randomized to receive placebo to match ambrisentan for 48 weeks, then transition to ambrisentan treatment at the initial dose of 5 mg for 4 weeks, followed by ambrisentan at the target dose of 10 mg for an additional 4 weeks.