Long-term Safety and Efficacy of Efanesoctocog Alfa (BIVV001) in Previously Treated Patients With Hemophilia A (XTEND-ed)
Hemophilia A
About this trial
This is an interventional treatment trial for Hemophilia A
Eligibility Criteria
Inclusion criteria :
For participants rolling over into Arm A
- Participants who have completed the studies EFC16923, EFC16925, Arm B or Arm C of the current study, or any other potential BIVV001 study.
- Male or Female For participants new to BIVV001 (Arm B and C)
- Participants who have severe hemophilia A, defined as <1 IU/dL (<1%) endogenous FVIII activity as documented either by central laboratory testing at screening or in historical medical records from a clinical laboratory demonstrating <1% FVIII coagulant activity (FVIII:C) or a documented genotype known to produce severe hemophilia A.
- Previous treatment for hemophilia A (prophylaxis or on-demand) with any recombinant and/or plasma-derived FVIII, or cryoprecipitate for at least 150 EDs or 50 EDs for participants aged <6 years.
- Platelet count ≥100 000 cells/μL at screening.
- A participant known to be human immunodeficiency virus (HIV) antibody positive, either previously documented or identified from screening assessments, must have the following results prior to enrollment: CD4 lymphocyte count >200 cells/mm³ and viral load of <400 000 copies/mL
- Male
- Only for Arm B: Chinese participants
- Only for Arm C: planned major surgery within 6 months after Day 1.
Exclusion criteria:
For participants rolling over into Arm A
- Positive inhibitor result, defined as ≥0.6 Bethesda units (BU)/mL.
- Participation in another study. For participants new to BIVV001 (Arm B and Arm C)
- Any concurrent clinically significant liver disease that, in the opinion of the Investigator, would make the participant unsuitable for enrollment. This may include, but is not limited to cirrhosis, portal hypertension, and acute hepatitis.
- Serious active bacterial, fungal, or viral infection (other than chronic hepatitis or HIV) present within 30 days of screening.
- Other known coagulation disorder(s) in addition to hemophilia A.
- History of hypersensitivity or anaphylaxis associated with any FVIII product.
- History of a positive inhibitor (to FVIII) test defined as ≥0.6 BU/mL, or any value greater than or equal to the lower sensitivity cut-off for laboratories with cut-offs for inhibitor detection between 0.7 and 1.0 BU/mL, or clinical signs or symptoms of decreased response to FVIII administrations. Family history of inhibitors will not exclude the participant.
- Positive inhibitor test (FVIII) result, defined as ≥0.6 BU/mL at screening.
- Treatment with acetylsalicylic acid (ASA) or antiplatelet agents that are not nonsteroidal anti-inflammatory drugs (NSAIDs) within 2 weeks prior to screening.
- Treatment with NSAIDs greater than the maximum dose specified in the regional prescribing information within 2 weeks prior to screening.
- Systemic treatment within 12 weeks prior to Screening with chemotherapy and/or other immunosuppressive drugs (except for the treatment of hepatitis C virus [HCV] or HIV).
- Emicizumab use within the 20 weeks prior to screening.
- Major surgery within 8 weeks prior to screening.
The above information is not intended to contain all considerations relevant to a patient's potential participation in a clinical trial.
Sites / Locations
- Orthopaedic Institute for Children-Site Number:8400003
- Children's Hospital Los Angeles-Site Number:8400009
- University of California San Diego-Site Number:8400007
- University of Florida Health-Site Number:8400008
- Children's Healthcare of Atlanta-Site Number:8400016
- Rush University Medical Center-Site Number:8400010
- Children's Hospital Of Iowa-Site Number:8400011
- University of Michigan Medical Center-Site Number:8400006
- Michigan State University School Of Med-Site Number:8400002
- Hemostasis and Thrombosis Center of Nevada-Site Number:8400001
- New York Presbyterian Hospital/Weill Cornell Medical Center-Site Number:8400017
- East Carolina University -2390 Hemby Ln-Site Number:8400015
- Cincinnati Children's Hospital Medical Center-Site Number:8400012
- Children's Research Institute-Site Number:8400013
- Bloodworks Northwest-Site Number:8400005
- Children's Hospital Of Wisconsin-Site Number:8400014
- Investigational Site Number :0320001
- Investigational Site Number :0320002
- Investigational Site Number :0320003
- Investigational Site Number :0360004
- Investigational Site Number :0360001
- Investigational Site Number :0360002
- Investigational Site Number :0360003
- Investigational Site Number :0560003
- Investigational Site Number :0760001
- Investigational Site Number :1000171
- Investigational Site Number :1000172
- Investigational Site Number :1240005
- Investigational Site Number :1240004
- Investigational Site Number :1240002
- Investigational Site Number :1240001
- Investigational Site Number :1560006
- Investigational Site Number :1560002
- Investigational Site Number :1560001
- Investigational Site Number :1560003
- Investigational Site Number :1560004
- Investigational Site Number :1560005
- Investigational Site Number :1560009
- Investigational Site Number :1560010
- Investigational Site Number :1560013
- Investigational Site Number :1560007
- Investigational Site Number :2500005
- Investigational Site Number :2500004
- Investigational Site Number :2500001
- Investigational Site Number :2500003
- Investigational Site Number :2500006
- Investigational Site Number :2760304
- Investigational Site Number :2760302
- Investigational Site Number :2760001
- Investigational Site Number :2760002
- Investigational Site Number :3000001
- Investigational Site Number :3480002
- Investigational Site Number :3480004
- Investigational Site Number :3480005
- Investigational Site Number :3720001
- Investigational Site Number :3800002
- Investigational Site Number :3800001
- Investigational Site Number :3800003
- Investigational Site Number :3920425
- Investigational Site Number :3920423
- Investigational Site Number :3920426
- Investigational Site Number :3920422
- Investigational Site Number :3920421
- Investigational Site Number :3920424
- Investigational Site Number :4100603
- Investigational Site Number :4100601
- Investigational Site Number :4100600
- Investigational Site Number :5280002
- Investigational Site Number :5280001
- Investigational Site Number :7240002
- Investigational Site Number :7240001
- Investigational Site Number :7520001
- Investigational Site Number :7560001
- Investigational Site Number :1580005
- Investigational Site Number :1580001
- Investigational Site Number :1580003
- Investigational Site Number :1580002
- Investigational Site Number :1580004
- Investigational Site Number :7920004
- Investigational Site Number :7920001
- Investigational Site Number :7920003
- Investigational Site Number :8260005
- Investigational Site Number :8260001
- Investigational Site Number :8260003
- Investigational Site Number :8260004
Arms of the Study
Arm 1
Arm 2
Arm 3
Experimental
Experimental
Experimental
Arm A: Previously treated in BIVV001 study
Arm B: Newly initiated (China Only) in BIVV001
Arm C: Newly initiated in BIVV001 with planned major surgery
This arm includes all participants who have completed the previous phase 3 studies on BIVV001, as well as participants who have completed Arm B or Arm C of this study rolling over in Arm A, and participants who will have completed any future BIVV001 study who will be proposed to continue BIVV001 treatment. Participants in this arm will continue receiving BIVV001 prophylaxis treatment once-weekly (QW) for a total of 100 exposure days (EDs) cumulative from the parent study and this study. Participants will have the opportunity to continue in this study for up to 4 years, unless BIVV001 is commercially available in their applicable participating country.
This arm includes Chinese participants of any age who will be newly initiated on BIVV001 prophylaxis treatment once-weekly (QW) for 52 weeks. After 52 weeks of treatment in this arm B, participants will be able to roll into arm A.
This arm includes participants of any age who will be newly initiated on BIVV001 prophylaxis treatment once-weekly (QW) and will undergo planned major surgery after at least 6 initial EDs with BIVV001, and within 26 weeks from Day 1. After 52 weeks of treatment in arm C, participants will be able to roll into arm A.