Study of Oral Ixazomib in Adult Participants With Relapsed or Refractory Light Chain Amyloidosis
Light-Chain Amyloidosis
About this trial
This is an interventional treatment trial for Light-Chain Amyloidosis focused on measuring Drug therapy
Eligibility Criteria
Inclusion Criteria:
- Male or female participants 18 years or older
- Biopsy-proven systemic relapsed or refractory light-chain (AL) amyloidosis, which after at least 1 prior therapy, in the investigator's opinion, requires further treatment
- If received stem cell transplant, must be at least 3 months posttransplantation and recovered from side effects
- Must have measurable disease defined as serum differential free light chain concentration ≥ 40 mg/L
- Must have objective measurable organ (heart or kidney) amyloid involvement
- Must have cardiac biomarker risk stage I or II disease
- Must have adequate hematologic, hepatic, and renal function
- Eastern Cooperative Oncology Group (ECOG) performance status of 0 to 2
- Female participants who are postmenopausal, surgically sterile, or agree to practice 2 effective methods of contraception or agree to abstain from heterosexual intercourse
- Male participants who agree to practice effective barrier contraception or agree to abstain from heterosexual intercourse
- Voluntary written consent
Exclusion Criteria
- Peripheral neuropathy that is greater or equal to Grade 2
- Cardiac status as described in protocol
- Severe diarrhea (≥ Grade 3) not controllable with medication or requires administration of total parenteral nutrition
- Known gastrointestinal condition or procedure that could interfere with swallowing or the oral absorption of tolerance of MLN9708
- Uncontrolled infection requiring systematic antibiotics
- Known human immunodeficiency virus (HIV) positive, hepatitis B surface antigen-positive status, or known or suspected active hepatitis C infection
- Presence of other active malignancy with the exception of nonmelanoma skin cancer, cervical cancer, treated early-stage prostate cancer provided that prostate-specific antigen is within normal limit, or any completely resected carcinoma in situ
- Female participants who are lactating or pregnant
- Major surgery within 14 days before the first dose of study drug
- Serious medical or psychiatric illness that could, in the investigator's opinion, potentially interfere with the completion of treatment according to the protocol
Sites / Locations
- Tufts Medical Center
- Boston Medical Center
- Barbara Ann Karmanos Cancer Institute
- Mayo Clinic
- Mount Sinai Medical Center
- Fox Chase Cancer Center
- University Health Network
- CHU Limoges, Department of Hematology and Cell Therapy, Reference Center for AL amyloidosis
- Universitatsklinikum Heidelberg Innere Medizin V; Hamatologie, Onkologie und Rheumatologie
- Amyloidosis Research & Treatment Center, Fondazione IRCCS Policlinico San Matteo
Arms of the Study
Arm 1
Arm 2
Arm 3
Arm 4
Experimental
Experimental
Experimental
Experimental
Dose Escalation Cohort: Ixazomib 4.0 mg
Dose Escalation Cohort: Ixazomib 5.5 mg
Dose Expansion Cohort: Ixazomib 4.0 mg (PI Naive)
Dose Expansion Cohort: Ixazomib 4.0 mg (PI Exposed)
Ixazomib 4.0 mg, capsule, orally, once weekly on Days 1, 8 and 15 during each 28-day treatment cycle for 3 cycles. If there was no hematologic response, dexamethasone 40 mg, tablet, orally was added once on Days 1 to 4 of every cycle, beginning in Cycle 4 for 3 additional cycles. If there was no hematologic response the participant was discontinued. Participants with hematologic response continued treatment up to maximum 12 cycles.
Ixazomib 5.5 mg, capsule, orally, once weekly on Days 1, 8 and 15 during each 28-day treatment cycle for 3 cycles. If there was no hematologic response, dexamethasone 40 mg, tablet, orally was added once on Days 1 to 4 of every cycle, beginning in Cycle 4 for 3 additional cycles. If there was no hematologic response the participant was discontinued. Participants with hematologic response continued treatment up to maximum 12 cycles.
Ixazomib 4.0 mg, capsule, orally, on Days 1, 8 and 15 during a 28-day treatment cycle until progressive disease (PD) or unacceptable toxicity, for participants with relapsed or refractory amyloidosis and who were not treated with any other proteasome inhibitor (PI). Duration of treatment was up to 12 months unless the investigator and sponsor determined the participant would benefit from therapy beyond 12 months.
Ixazomib 4.0 mg, capsule, orally, on Days 1, 8 and 15 during a 28-day treatment cycle until PD or unacceptable toxicity, for participants with relapsed or refractory amyloidosis and who were previously treated with any other PI. Duration of treatment was up to 12 months unless the investigator and sponsor determined the participant would benefit from therapy beyond 12 months.