Study of Venetoclax and Azacitidine in Advanced BCR-ABL Negative Myeloproliferative Neoplasms
Myeloproliferative Neoplasm
About this trial
This is an interventional treatment trial for Myeloproliferative Neoplasm
Eligibility Criteria
Inclusion Criteria:
- Ability to voluntarily provide written informed consent.
- Documented diagnosis per World Health Organization (WHO) 2016 criteria of BCR-ABL negative myeloproliferative neoplasms (MPN).
- Documented MPN transformation to accelerated phase (AP) or blast phase (BP) without prior blast reduction therapy for their AP/BP disease.
- Eastern Cooperative Oncology Group (ECOG) performance status 0-2.
- Adequate organ function.
- Must practice at least one reliable method of birth-control starting at least on cycle 1 day 1 until at least 90 days after the last dose of study drug.
- Female participants of childbearing potential must have a negative serum pregnancy test within 14 days prior to cycle 1 day 1.
Exclusion Criteria:
- History of allogeneic stem cell transplant for MPN.
- Previous treatment with venetoclax, navitoclax, azacytidine or other hypomethylating agents (HMA).
- White blood cell count >25 x 10^9/L.
- Current enrollment in another interventional study.
- Presence of any active uncontrolled infection such as bacterial or fungal infections progressing despite adequate antimicrobial treatment.
- Myocardial infarction in the preceding 3 months.
- Active human immunodeficiency virus (HIV), hepatitis B (HBV), hepatitis C (HCV) infection.
- History of active malignancy in the previous 2 years.
- Any psychiatric illness or social circumstances or significant co-morbid conditions that may compromise study participation.
- Pregnant or breastfeeding women.
- Patients with known central nervous system (CNS) involvement with acute myeloid leukemia (AML) or CNS extramedullary hematopoiesis.
- Patients with t (15;17)
- Patients who have received strong and/or moderate CYP3A inducers within 7 days prior to the initiation of study treatment.
- Active COVID-19 infection.
- History of prior blast-reduction therapy for AP/BP-MPN.
- Preceding history MDS, chronic myelomonocytic leukemia (CMML), and other myelodysplastic syndromes (MDS)/MPN overlap syndromes.
Sites / Locations
- Princess Margaret Cancer Centre
Arms of the Study
Arm 1
Experimental
Azacitidine and Venetoclax
A treatment cycle is 28 days long. Azacitidine will be given by injection under the skin, once a day, for the first 6 days of every cycle. Venetoclax will be given orally, once a day, as follows at the discretion of their study doctors: Cycle 1: Day 1 - 100 mg Day 2 - 200 mg Days 3 to 28 - 400 mg Cycle 2: Participants with a response to the study drugs will continue taking 400 mg from Days 1 to 21, with no study drug from Days 22 to 28 during Cycle 2. Participants who have not yet responded to the study drugs will continue taking 400 mg from Days 1 to 28 during Cycle 2. Cycle 3 and subsequent cycles: Participants with a response to the study drugs will continue to take 400 mg from Days 1 to 21, with no study drug from Days 22 to 28. Participants whose disease has not worsened will continue taking 400 mg from Days 1 to 28. Participants have not responded to the study drugs will be withdrawn from the study.