Treatment of Bardet-Biedl-Syndrome With Metformin for Evaluation of a Possible Visual Improvement (BBS)
Primary Purpose
Bardet-Biedl Syndrome, Visual Impairment
Status
Withdrawn
Phase
Phase 2
Locations
Study Type
Interventional
Intervention
Metformin
Sponsored by
About this trial
This is an interventional treatment trial for Bardet-Biedl Syndrome
Eligibility Criteria
Inclusion Criteria:
- clinically confirmed Bardet-Biedl-syndrome
- Visual acuity between 0.05 and 0.8
- Age >=10 year to <25 years
- Visual field III4e or V4e with diameter >=5°, if II4e not seen
- informed consent of patient and/or legal representative
Exclusion Criteria:
- Hypoglycaemia (<50mg/dl)
- Therapy with Metformin within the last three months
- Participation in another clinical trial
- pregnancy, lactation
- any contra indication concerning Metformin therapy
- Renal failure (creatinine clearance < 60ml/min)
- any acute disorder accompanied by clouding of consciousness
- acute or chronic disorders possible accompanied by tissue hypoxia
- Liver insufficiency, alcohol abuse
- not fluent in German language
Sites / Locations
Arms of the Study
Arm 1
Arm Type
Experimental
Arm Label
Metformin Therapy
Arm Description
Metformin therapy once daily for 24 weeks with a dose of 500, 850 or 1000 mg depending on body weight
Outcomes
Primary Outcome Measures
Visual acuity
Course of visual acuity according to appropriate table
Secondary Outcome Measures
Number of letters read
Course visual acuity defined as number of letters read
Results of Static perimetry
Course of results of static perimetry given by measurement of light contrast sensitivity within at least 5 central points.
Results of Kinetic perimetry
Course of results of kinetic perimetry given by mapping the visual field sensitivity boundaries using Goldmann perimetry
Electroretinogram (ERG) dim-flash
Course of values of ERG dim-flash
Electroretinogram (ERG) standard flash
Course of values of ERG standard flash at 3 ods/m2
Electroretinogram (ERG) cone-single-flash
Course of values of ERG cone-single-flash at 30cd/m2
Electroretinogram (ERG) 30-Hz-Flicker
Course of values of ERG measured by 30-Hz-Flicker in all patients
Visual evoked potential (VEP) - amplitude
Course of results of measurement of VEP amplitude
Visual evoked potential (VEP) - latency time
Course of results of measurement of VEP latency time
FST
Full-Field-Stimulus Threshold
optical coherence tomography (OCT)
Course of central thickness of retina measured by OCT
Full Information
NCT ID
NCT03490019
First Posted
March 19, 2018
Last Updated
April 16, 2019
Sponsor
University Hospital Tuebingen
1. Study Identification
Unique Protocol Identification Number
NCT03490019
Brief Title
Treatment of Bardet-Biedl-Syndrome With Metformin for Evaluation of a Possible Visual Improvement
Acronym
BBS
Official Title
Treatment of Infantile and Juvenile Patients With Bardet-Biedl-Syndrome With Metformin. Evaluation of a Visual Improvement as a Side Effect of the Pediatric Treatment of Adipositas - a Prospective Pilot Study Without Control
Study Type
Interventional
2. Study Status
Record Verification Date
February 2018
Overall Recruitment Status
Withdrawn
Why Stopped
unrealizable wishes of national authorities
Study Start Date
April 1, 2018 (Anticipated)
Primary Completion Date
October 2019 (Anticipated)
Study Completion Date
August 2020 (Anticipated)
3. Sponsor/Collaborators
Responsible Party, by Official Title
Sponsor
Name of the Sponsor
University Hospital Tuebingen
4. Oversight
Studies a U.S. FDA-regulated Drug Product
No
Studies a U.S. FDA-regulated Device Product
No
Data Monitoring Committee
Yes
5. Study Description
Brief Summary
In this prospective pilot study without control group children and young adults (10-25 years old) diagnosed with Bardet-Biedl syndrome and treated with Metformin for their adipositas will be evaluated for a possible additional effect of Metformin on visual acuity.
Detailed Description
Within experiments with animals a positive effect of Metformin concerning the photo receptors was shown. Several patients of the university hospital Tübingen with Bardet-Biedl-Syndrome and Metformin therapy due to their adipositas reported a subjective improvement of the visual acuity which was confirmed by opthalmologic tests.
This will be checked in a prospective pilot study without control group including children and young adults (10-25 years old) diagnosed with Bardet-Biedl syndrome and treated with Metformin for their adipositas. Therefore a possible additional effect of Metformin on visual acuity will be evaluated under controlled conditions.
6. Conditions and Keywords
Primary Disease or Condition Being Studied in the Trial, or the Focus of the Study
Bardet-Biedl Syndrome, Visual Impairment
7. Study Design
Primary Purpose
Treatment
Study Phase
Phase 2
Interventional Study Model
Single Group Assignment
Model Description
Prospective pilot study without control group
Masking
None (Open Label)
Allocation
N/A
Enrollment
0 (Actual)
8. Arms, Groups, and Interventions
Arm Title
Metformin Therapy
Arm Type
Experimental
Arm Description
Metformin therapy once daily for 24 weeks with a dose of 500, 850 or 1000 mg depending on body weight
Intervention Type
Drug
Intervention Name(s)
Metformin
Intervention Description
500, 850 or 1000 mg depending on body weight once daily for 24 weeks
Primary Outcome Measure Information:
Title
Visual acuity
Description
Course of visual acuity according to appropriate table
Time Frame
Baseline to day 210
Secondary Outcome Measure Information:
Title
Number of letters read
Description
Course visual acuity defined as number of letters read
Time Frame
Baseline to day 210
Title
Results of Static perimetry
Description
Course of results of static perimetry given by measurement of light contrast sensitivity within at least 5 central points.
Time Frame
Baseline to day 210
Title
Results of Kinetic perimetry
Description
Course of results of kinetic perimetry given by mapping the visual field sensitivity boundaries using Goldmann perimetry
Time Frame
Baseline to day 210
Title
Electroretinogram (ERG) dim-flash
Description
Course of values of ERG dim-flash
Time Frame
Baseline to day 210
Title
Electroretinogram (ERG) standard flash
Description
Course of values of ERG standard flash at 3 ods/m2
Time Frame
Baseline to day 210
Title
Electroretinogram (ERG) cone-single-flash
Description
Course of values of ERG cone-single-flash at 30cd/m2
Time Frame
Baseline to day 210
Title
Electroretinogram (ERG) 30-Hz-Flicker
Description
Course of values of ERG measured by 30-Hz-Flicker in all patients
Time Frame
Baseline to day 210
Title
Visual evoked potential (VEP) - amplitude
Description
Course of results of measurement of VEP amplitude
Time Frame
Baseline to day 210
Title
Visual evoked potential (VEP) - latency time
Description
Course of results of measurement of VEP latency time
Time Frame
Baseline to day 210
Title
FST
Description
Full-Field-Stimulus Threshold
Time Frame
Baseline to day 210
Title
optical coherence tomography (OCT)
Description
Course of central thickness of retina measured by OCT
Time Frame
Baseline to day 210
10. Eligibility
Sex
All
Minimum Age & Unit of Time
10 Years
Maximum Age & Unit of Time
25 Years
Accepts Healthy Volunteers
No
Eligibility Criteria
Inclusion Criteria:
clinically confirmed Bardet-Biedl-syndrome
Visual acuity between 0.05 and 0.8
Age >=10 year to <25 years
Visual field III4e or V4e with diameter >=5°, if II4e not seen
informed consent of patient and/or legal representative
Exclusion Criteria:
Hypoglycaemia (<50mg/dl)
Therapy with Metformin within the last three months
Participation in another clinical trial
pregnancy, lactation
any contra indication concerning Metformin therapy
Renal failure (creatinine clearance < 60ml/min)
any acute disorder accompanied by clouding of consciousness
acute or chronic disorders possible accompanied by tissue hypoxia
Liver insufficiency, alcohol abuse
not fluent in German language
Overall Study Officials:
First Name & Middle Initial & Last Name & Degree
Heiko Billing, PD Dr. med.
Organizational Affiliation
Universtitätsklinikum Tübingen
Official's Role
Principal Investigator
12. IPD Sharing Statement
Plan to Share IPD
Undecided
Learn more about this trial
Treatment of Bardet-Biedl-Syndrome With Metformin for Evaluation of a Possible Visual Improvement
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